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Case: The objective is to present the successful experience of multidisciplinary management of a patient with short bowel syndrome and intestinal failure with progression to intestinal adaptation.
This is a newly born premature with intestinal atresia type IV with multiple intestinal atresia who evolved to intestinal failure and required managed with prolonged parenteral nutritional support, multiple antibiotic schemes, prebiotics, multivitamins, enteral nutrition with elemental formula to achieve their adaptation intestinal until lead to a normal diet. The evolution of these patients intestinal failure is a challenge for the health team, as it not only involves the surgical
management of your condition if not basic nutritional support, fluid and electrolyte balance, hepatic dysfunction cholestasis associated infections etc. Discussion: Short bowel syndrome with progression to intestinal failure in children is a condition whose prevalence is increasing worldwide, thanks to advances in neonatal intensive care, neonatal surgery, and nutritional support of patients with conditions such as gastroschisis, omphalocele and necrotizing enterocolitis. Despite the limitations of our health system, it is possible to offer a multidisciplinary and integrated to lead to intestinal adaptation treatment.

Ramírez Prada, D., & del Castillo Calderón, G. (2015). Short Bowel Syndrome, a Case of Intestinal Rehabilitation. Revista Ciencias De La Salud, 13(02), 309–316. https://doi.org/10.12804/revsalud13.02.2015.12

Valdovinos D, Cadena J, Montijo E, Zarate F, Cazares M, Toro E, et al. Sindrome de intestino corto en ninos, actualidades en su diagnostico y manejo. Rev Gastroenterol Mex. 2012;77(3):130-140.

Sigalet D, Boctor D, Robertson M, Lam V, Brindle M, Sarkhosh K, et al. Improved outcomes in paediatric intestinal failure with aggressive prevention of liver disease. Eur J Pediatr Surg. 2009;19: 348-353.

Khalil BA, Ba’ath ME, Aziz A, Forsythe L, Gozzini S, Murphy F, et al. Intestinal rehabilitation and bowel reconstructive surgery: improved outcomes in children with short bowel syndrome. J Pediatr Gastroenterol Nutr. 2012;54(4):505-509.

Wessel JJ, Kocoshsis SA. Nutritional management of infants with short bowel syndrome. Semin Perinatol. 2007;31(2):104-111.

Theyskens C, Dams A. Enteral nutrition regimen for neonates with short bowel syndrome. Nutrition. 2008;24(10):1045-1047.

Soler-Palacin P, Garzon-Lorenzo P, Castilla-Fernandez Y, Arranz Amo JA, Scheider S, Tormo Carnice R, et al. Acidosis D-lactica en un paciente de 11 anos con sindrome de intestino corto. An Pediatr (Barc). 2006;64(4):385-387.

Diamanti A, Conforti A, Panetta F, Torre G, Candusso M, Bagolan P, et al. Long-term outcome of home parenteral nutrition in patients with ultra-short bowel syndrome. J Pediatr Gastroenterol Nutr 2014;58(4):438-42.

Avitzur Y, Grant D. Intestine Transplantation in Children: Update 2010. Pediatr Clin North Am. 2010;57(2):415-31.

Wales PW, Allen N, Worthington P, George D, Compher C. The American Society for Parenteral and Enteral Nutrition, Teitelbaum D. A.S.P.E.N. Clinical Guidelines: Support of Pediatric Patients With Intestinal Failure at Risk of Parenteral Nutrition-Associated Liver Disease. JPEN J Parenter Enteral Nutr. 2014;38(5):538-557.

Correa C, Mallarino C, Pena R, Rincon LC, Gracia G, Zarante I. Congenital malformations of pediatric surgical interest: prevalence, risk factors, and prenatal diagnosis between 2005 and 2012 in the capital city of a developing country. Bogota, Colombia. J Pediatr Surg. 2014;49(7):1099-1103.

Alvarado-Socarras J, Rodriguez SC. Acrodermatitis enteropathica associated with short bowel syndrome. An Pediatr (Barc). 2013;79(3):191-192.

Schalamon J, Mayr JM, Hollwarth ME. Mortality and economics in short bowel syndrome. Best Pract Res Clin Gastroenterol 2003;17(6):931-942.

Fishbein TM, Matsumoto CS. Intestinal replacement therapy: Timing and indications for referral of patients to an intestinal rehabilitation and transplant program. Gastroenterology 2006;130: S147–151.

Nasr A, Avitzur Y, Ng VL, De Silva N, Wales PW. The use of hyperbilirubinemia (>100 mmol/L) as an indicator of irreversible liver disease in infants with short bowel syndrome. J Pediatr Surg 2007;42(2):359-362.

Gutierrez IM, Kang KH, Jaksic T. Neonatal short bowel syndrome. Semin Fetal Neonatal Med 2011;16(3):157-163.

Gong JF, Zhu WM, Yu WK, Li N, Li JS. Role of enteral nutrition in adult short bowel syndrome undergoing intestinal rehabilitation: the long-term outcome. Asia Pac J Clin Nutr. 2009;18(2):155-163.

Dobson R, McGuckin C, Walker G, Lucas C, McGrogan P, Russell RK, et al. Cycled enteral antibiotics reduce sepsis rates in paediatric patients on long-term parenteral nutrition for intestinal failure. Aliment Pharmacol Ther 2011;34:1005-1011.

Craig R, Ehrenpreis E. D-xylose testing. J Clin Gastroenterol. 1999;29(2):143-150.

Javid PJ, Malone FR, Reyes J, Healey PJ, Horslen SP. The experience of a regional pediatric intestinal failure program: Successful outcomes from intestinal rehabilitation. Am J Surg 2010;199(5):676-679.

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